Cardiovascular

Left pulmonary artery sling in an infant: a vascular anomaly with a high impact on breathing.

TL;DR

Surgical reimplantation of the left pulmonary artery to the main pulmonary artery with concurrent slide tracheoplasty resulted in full recovery in an infant with left pulmonary artery sling causing significant tracheal compression.

Key Findings

Left pulmonary artery sling was identified as the cause of persistent stridor and recurrent respiratory distress in an infant presenting since birth.

  • The patient was an infant with symptoms present from birth
  • Clinical presentation included persistent stridor and recurrent respiratory distress
  • Imaging was used to confirm the diagnosis of left pulmonary artery sling
  • The anomaly caused significant tracheal compression

Surgical reimplantation of the left pulmonary artery to the main pulmonary artery combined with concurrent slide tracheoplasty resulted in full recovery.

  • The surgical approach involved reimplantation of the left pulmonary artery to the main pulmonary artery
  • Slide tracheoplasty was performed concurrently to address tracheal compression
  • The outcome was described as full recovery
  • This is a case report describing a single patient

Early recognition of vascular anomalies is highlighted as important in infants presenting with unexplained airway obstruction.

  • The case illustrates that left pulmonary artery sling can present as unexplained airway obstruction in infants
  • The authors emphasize the high impact of this vascular anomaly on breathing
  • Imaging was necessary to reveal the underlying vascular cause of respiratory symptoms
  • The case underscores the need for vascular anomalies to be considered in the differential diagnosis of infant stridor

What This Means

This case report describes an infant who had noisy breathing (stridor) and repeated breathing difficulties from birth. Medical imaging revealed an unusual blood vessel arrangement called a left pulmonary artery sling, where the left pulmonary artery takes an abnormal path that wraps around and squeezes the windpipe (trachea), making it hard for the baby to breathe normally. The infant underwent surgery in which the misplaced artery was detached and reattached in its correct position, and a procedure called a slide tracheoplasty was performed at the same time to repair the compressed and narrowed section of the windpipe. Following these combined procedures, the infant made a full recovery. This research suggests that when babies have unexplained noisy or difficult breathing that starts at birth, doctors should consider the possibility of abnormal blood vessel arrangements as the underlying cause. Left pulmonary artery sling is a rare but serious condition that can be effectively treated with surgery when identified early, and this case illustrates the importance of using imaging to look for vascular causes of airway problems in infants.

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Citation

Bizhga M, Saraci B. (2026). Left pulmonary artery sling in an infant: a vascular anomaly with a high impact on breathing.. BMJ case reports. https://doi.org/10.1136/bcr-2025-271605