Cardiovascular

Post pulmonary embolism syndrome following paediatric pulmonary embolism: a multicentre, retrospective cohort study.

TL;DR

Post pulmonary embolism syndrome showed a high prevalence in children, occurring in 35% at 3 months, 24% at 1 year, and 16% at 2 years, with incomplete thrombus resolution, PICU admission, intermediate/high-risk PE, comorbidity, ongoing treatment, and psychological distress identified as clinical factors associated with physical limitations.

Key Findings

Post pulmonary embolism syndrome (PPES) was highly prevalent in children following pulmonary embolism, affecting 35% at 3 months, 24% at 1 year, and 16% at 2 years.

  • 63 of 178 patients (35%) developed PPES at 3 months post pulmonary embolism
  • 41 of 168 patients (24%) had PPES at 1 year follow-up
  • 25 of 161 patients (16%) had PPES at 2 years follow-up
  • Overall, 63 (35%) patients developed PPES within 2 years, while 115 (65%) did not
  • Follow-up completion was high: 100% at 3 months, 94% at 1 year, and 93% at 2 years

Incomplete thrombus resolution was significantly associated with physical limitations at 1 year post pulmonary embolism.

  • Odds ratio 3.8 (95% CI 1.4–10.3), p=0.0090
  • This was identified through multivariate analysis with confounders determined using directed acyclic graph methodology
  • Physical restriction at 1 year post pulmonary embolism was the secondary outcome measure

Intermediate-risk or high-risk pulmonary embolism classification was the strongest clinical factor associated with physical limitations at 1 year.

  • Odds ratio 4.1 (95% CI 1.8–9.4), p=0.0010
  • This was among the highest odds ratios of all factors examined
  • Identified via multivariate analysis adjusting for confounders

Psychological distress at 3 months post pulmonary embolism was strongly associated with physical limitations at 1 year.

  • Odds ratio 4.3 (95% CI 1.9–9.8), p=0.0010
  • This was the highest odds ratio among all identified clinical factors
  • Findings emphasise the need for comprehensive, multidisciplinary care including psychological support

PICU admission was independently associated with physical limitations at 1 year post pulmonary embolism.

  • Odds ratio 2.8 (95% CI 1.2–7.6), p=0.017
  • Identified as one of six clinical factors associated with physical restriction at 1 year
  • Multivariate analysis was used to control for confounders

Presence of comorbidity and ongoing anticoagulation treatment were each associated with physical limitations at 1 year.

  • Comorbidity: OR 2.9 (95% CI 1.3–6.4), p=0.010
  • Ongoing treatment: OR 2.8 (95% CI 1.2–6.5), p=0.016
  • Both factors were identified in the same multivariate analysis framework

Regular exercise at least 3 times per week was inversely associated with physical limitations at 1 year post pulmonary embolism.

  • Odds ratio 0.31 (95% CI 0.1–0.8), p=0.0090
  • This was the only factor identified as protective against physical limitations
  • Identified through the same multivariate analysis as the risk factors

The study cohort consisted predominantly of adolescent female patients treated at six tertiary paediatric hospitals in the Netherlands from 2012 to 2022.

  • 183 patients were initially eligible; 178 were included after exclusions (4 for insufficient follow-up data, 1 death)
  • 115 (65%) were female and 63 (35%) were male
  • Median age was 15.0 years (IQR 13.0–16.0)
  • This was a multicentre, retrospective cohort study

What This Means

This research suggests that a significant proportion of children who experience a pulmonary embolism (a blood clot in the lungs) go on to develop 'post pulmonary embolism syndrome' (PPES) — a condition involving ongoing physical and psychological difficulties after the initial clot. Studying 178 children treated at six Dutch hospitals over a decade, the researchers found that 35% had PPES at 3 months after their clot, dropping to 24% at 1 year and 16% at 2 years. This indicates that while many children improve over time, a meaningful number continue to experience lasting effects. The study identified several factors that increased the likelihood of physical limitations one year after the pulmonary embolism. Children who had more severe clots (classified as intermediate or high risk), were admitted to intensive care, had other health conditions, still needed treatment at follow-up, had incomplete resolution of their clot, or experienced psychological distress at 3 months were all more likely to have physical limitations at 1 year. Notably, psychological distress and PE severity had the strongest associations. On the positive side, children who exercised at least three times per week were significantly less likely to have physical limitations. This research suggests that recovery from childhood pulmonary embolism is not just a physical process — psychological wellbeing and activity levels also play important roles. The findings point to the value of comprehensive, multidisciplinary follow-up care for children after a pulmonary embolism, incorporating both physical and psychological support, rather than focusing solely on the clot itself.

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Citation

Verweij M, van Ommen C, Diender M, Jongmans-van der Heide A, Hovinga I, Rettenbacher E, et al.. (2026). Post pulmonary embolism syndrome following paediatric pulmonary embolism: a multicentre, retrospective cohort study.. The Lancet. Haematology. https://doi.org/10.1016/S2352-3026(26)00071-2